Bladder exstrophy is a rare birth defect in which the anterior wall of the
abdomen over the bladder does not close during the intrauterine period,
leaving the child with an exposed bladder. Bladder exstrophy affects one out
of every 50,000 births. Possible complaints include exposed bladder,
incontinence or urine leakage, genital and pelvic bone defects, as well as
intestine and reproductive organ defects. The majority of patients have their
bladder exstrophy repaired as infants. If it is not addressed, as it was in this
case, staged surgery will be required. A three-year-old male child with
congenital bladder exstrophy was admitted to the Paediatric Surgeon's
Outpatient Department in this case. Orthopaedic surgeons were consulted
due to the pubic diastasis. At the age of three, an acetabulo-pelvic surgeon
recommends using an external fixator on the pelvic wings to reduce tension
on the reconstructed bladder wall and inter-pubic ligament. The patient was
treated for undiagnosed bladder exstrophy. The reconstruction of the
abdominal wall and urethra, as well as the use of an external fixator, was
completed.
Keywords: Bladder exstrophy, External fixation in pelvic wings, stage wise
surgery in neglected bladder exstrophy
