The exceptional cases of facial clefts are undoubtedly a surgical dogma to the surgeons. These cases bring the surgeon into a state of surgical muddle. The uniqueness of these defects demands a systematic multidisciplinary approach over a period of time. The identification of the type of cleft is critical in order to sketch out the treatment algorithm for that individual case. Therefore these extremely uncommon cases ought to be documented for further reference and enhancement of the literature available. To the best of our knowledge, this would be the sixth case of Tessier Cleft 1-13 to be documented.
Keywords: Tessier cleft 1-13, facial cleft, hypertelorism, encephalocele