Objective: To elucidate the challenges associated with anesthesia and successful
management strategies in a pregnant patient with severe pulmonary arterial
hypertension and Eisenmenger physiology undergoing cesarean section.
Background: Congenital heart disease is a leading cause of maternal cardiac
deaths, with Eisenmenger's syndrome being high-risk due to potential
complications. Pulmonary hypertension, characterized by an increase in mean
pulmonary artery pressure, is associated with a high mortality rate between 30%
and 56%. Advancements in medicine have improved the prognosis and quality of
life for patients with pulmonary arterial hypertension. However, managing
cesarean sections for parturients with Eisenmenger's syndrome remains
challenging. Case notes: A 27-year-old primigravida with severe pulmonary
arterial hypertension secondary to congenital heart disease, diagnosed with
Eisenmenger physiology, underwent an emergency cesarean section at 32 weeks
for optimal maternal and fetal outcomes. The multidisciplinary team opted for
careful pre-operative assessment and invasive monitoring along with epidural
anesthesia. Postoperatively, the patient faced complications, including
thrombocytopenia, hematoma, and a positive COVID-19 diagnosis, yet was
discharged in stable condition. Conclusion: Continuous vigilance throughout the
perioperative and postoperative phases is crucial for optimizing outcomes in
pregnant patients with Eisenmenger physiology. The successful outcome in this
high-risk case underscores the importance of advanced medical modalities and
multidisciplinary approaches in addressing the complexities of such pregnancies.
Keywords: Eisenmenger syndrome, pulmonary hypertension, cesarean section,
high-risk pregnancy
