Primary sarcoma of the heart is an exceptionally rare condition with grave prognosis. All cardiac tumours can cause life threatening
complications. Diagnosis is much more challenging as cases present with non-specific symptoms. In our case, a series of
investigations were made which ultimately led to our diagnosis of a right atrial sarcoma. Here, we recount a fatal case of a locally
invasive primary cardiac sarcoma originating from the right atrium and presenting with a cardiac tamponade.
Keywords: Primary Cardiac Sarcoma, Cardiac Tamponade, Myxoma