Introduction: Epidermolysis bullosa (EB) is a group of rare inherited disorders characterised by formation of blisters following minor
trauma to the skin or mucosal surfaces. There are four major forms of EB- simple, junctional, dystrophic and Kindler syndrome.
According to the form of EB, the oral and dental manifestations are varied in the frequency and severity. Case Report: A 6-years old
girl with a dystrophic form of EB was attended in our dental care centre in 2018. On examination, the child had multiple blisters on
her elbows, feet, knees. Clinical and radiographic examinations revealed multiple carious lesions affecting almost the present primary
dentition, with moderate gingival inflammation. Treatment: The patient had oral hygiene and dietary instructions, restorative dental
treatment, extraction of badly decayed teeth. The patient was routinely followed up every three months for up to 1 year. On the last
recall visit, the patent presented with good oral health status.
Keywords: Dystrophic Epidermolysis Bullosa, Blisters, Case Report